|
Descriptive statistics |
||||||||
| Origin |
Series |
n |
% Females |
% Definite diagnosis |
Median age (range) |
PRNP M129V genotype |
||
|
|
||||||||
| MM n (%) |
MV n (%) |
VV n (%) |
||||||
|
|
||||||||
| NL |
sCJD |
79 |
59 |
52 |
67 (34–87) |
48 (67) |
16 (22) |
8 (11) |
| controls |
309 |
56 |
N/A |
71 (55–93) |
135 (45) |
145 (48) |
23 (8) |
|
|
|
||||||||
| UK |
sCJD |
48 |
58 |
50 |
67 (49–81) |
22 (46) |
13 (27) |
13 (27) |
| vCJD |
52 |
31 |
74 |
25 (12–62) |
52 (100) |
0 (0) |
0 (0) |
|
|
|
||||||||
| Italy |
sCJD |
194 |
57 |
73 |
67 (35–87) |
141 (73) |
31 (16) |
22 (11) |
Sánchez-Juan et al. BMC Medical Genetics 2007 8:77 doi:10.1186/1471-2350-8-77 |
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