Table 3

Rare associations with IgG4-related conditions (Case reports)

Head and neck


Submandibular gland fibrosis

Pancreas[95], cholangitis[187,188], pseudotumour[189]

Parotid involvement

pancreas[171]

Sjögren's syndrome

Pancreas[171,190], RPF[164], BOOP[191]

Maculopathy

MFF[126]

Uveitis

RPF[192]

Conjunctiva

Pseudotumour[86]

Hashimoto's disease, Graves' disease

RPF[193]


Cardiovascular


Constrictive pericarditis

RPF[194]

Heart valves

RPF[20,22]

Mediastinal fibrosis

RPF[194-196]

Chronic periaortitis/aneurysm

RPF[197-205]

Vasculitis

RPF[125,206,207]

Occlusive phlebitis

MFF[149]

Intermittent claudication

RPF[208]


Rheumatology


Rheumatoid arthritis

BOOP[176], RPF[209]

Polymyalgia rheumatica

BOOP[210]

Ankylosing spondylitis

RPF[211]

Periarticular fibrosis

RPF[212]

Skeletal hyperostosis

RPF[213]

Dermatomyositis

Pseudotumour[88], BOOP[214]

Polymyositis

BOOP[191,215]

Scleroderma

RPF[216]


Other autoimmune conditions


Systemic lupus erythematosus

RPF[217]

Idiopathic thrombocytopenic purpura

RPF[218,219]

Haemolytic anaemia

Lung[220], cholangitis[221]


Central nervous system


Brain

PCG[107], xanthogranuloma[118,222]

Sella

MFF[124,126]

Spinal cord compression

RPF[223]


Gastrointestinal


Primary biliary cirrhosis

RPF[224], BOOP[176]

Mesentery

RPF[112,152,175,225], pseudotumour[102,153,155]

Bladder/pelvic mass

RPF[49,208,226,227]

Duodenal obstruction

RPF[228,229]

Portal hypertension

RPF[230]


Others


Familial multifocal fibrosclerosis Familial RPF

MFF[43] RPF[42]

Proliferative crescentic glomerulonephritis, membranous glomerulonephritis

RPF[231] RPF[232]

Interstitial nephritis

Pancreas[233]

Testicular involvement

RPF[126,234]


MFF, multifocal fibrosclerosis; RPF, retroperitoneal fibrosis; BOOP, bronchiolitis obliterans with organizing pneumonia; PCG, plasma-cell granuloma.

Neild et al. BMC Medicine 2006 4:23   doi:10.1186/1741-7015-4-23

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