Table 1

Systemic scoring system for SJIA patients.

Score

Severity level

Systemic symptoms


0

None

No active disease


1

Mild

Having any one of the following: rash, fevers < 10 days in the past month, ESR 40 to 90, platelets > 450,000


2

Moderate

Having at least three of the following: rash, fever > 10 days in the past month, WBC > 20,000, ESR > 90, platelets > 550,000, d-dimers 250 to 500, elevated fibrinogen


3

Severe

Having any one of the following symptoms: pneumonitis, percarditis, pleural effusion, Macrophage Activation Syndrome (MAS)


Ling et al. BMC Medicine 2012 10:125   doi:10.1186/1741-7015-10-125

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