Table 4

Incidence and outcome of GISTs from different population-based studies


Italy
Sweden [10]
USA [11]
Iceland [12]
Spain [13]

Covered population





     Area
Modena
Western Sweden
12 SEER registries
Iceland
Girona
     Population
633,993
1.3–1.6 million
38.7 million
300,000
553,661
     Period
1991–2004
1983–2000
1992–2000
1990–2003
1994–2001
Incidence





     Number of cases
124
288
1,458
114
46
     Crude rate#
1.42
1.45
n.a.
n.a.
n.a.
     World ASR#
0.66
n.a.
n.a.
1.1
0.65
     US 2000 ASR#
0.98
n.a.
0.68
n.a.
n.a.
5-years relative survival (%)





     All cases
65.8
n.a.
45
n.a.
74.7
     Very low risk
100
n.a.
n.a.
n.a.
94.9(a)
     Low risk
90.1
n.a.
n.a.
n.a.

     Intermediate risk
93.1
n.a.
n.a.
n.a.
100
     High risk
61.5(b)
n.a.
n.a.
n.a.
21.4
     Overly malignant
12.4
n.a.
n.a.
n.a.
n.a.

#per 100,000 inhabitants

(a)Very low risk + low risk groups

(b)Excluding overly malignant diseases

Mucciarini et al. BMC Cancer 2007 7:230   doi:10.1186/1471-2407-7-230