Table 1

Baseline characteristics of the enrolled population
Patients N = 28 Controls N = 13 P value
Mean (SD) Median (range)
Age 8.4 (1.6) 8.5 (5.6-12.0) 9.5 (2.8) 10.5 (5.5-12.5) 0.11
NS 24.2 (8.5) 27.5 (4–34) - -
6MWT (m) 361.2 (98.0) 386 (42–518) - -
10 M (s) 6.8 (6.3) 5.1 (3–36) - -
GOWERS (s) 8.0 (9.5) 4.7 (1–45) - -
Isometric KE (N) 56 (35) 53 (10–134) 310 (151) 251 (135–628.3) <0.01*
Isometric KF (N) 52 (20) 51 (14–93) 130 (55) 124 (60–225) <0.01*
Isocinetic KE (N) 59 (33) 51 (15–141) 276 (128) 260 (130–546) <0.01*
Isocinetic KF (N) 48 (20) 49 (10–100) 124 (46) 122 (59–223) <0.01*
EE (N) 26 (14) 24 (5–56) 101 (49) 94 (25–168) <0.01*
EF (N) 24 (10) 22 (7–46) 113 (57) 100 (55–225) <0.01*

*p values adjusted for age.

Abbreviations: NS = North Star Scale; 6MWT = 6-min walking test; KE = Knee Extension; KF = Knee Flexion; EE = Elbow Extension; EF = Elbow Flexion.

Lerario et al.

Lerario et al. BMC Neurology 2012 12:91   doi:10.1186/1471-2377-12-91

Open Data