Table 3

Polymorphisms identified for TSC1 and TSC2 in Taiwanese TSC population.

TSC1

Exon
Nucleotide change
Codon change
Polymorphism type
Frequency
Reported
Reference

Intron 3
c.106+15

Intron
13 (16 %)
N
This study
10
c.965 T>C
p.M322T
Missense
9 (11%)
R
[24]
Intron 11
c.1142-33 A>G

Intron
9 (11%)
R
LOVDa
Intron 12
c.1264-12 T>C

Intron
3 (4 %)
N
This study
Intron 14
c.1437-37 C>T

Intron
9 (11%)
R
LOVDa
15
c.1726 T>C
p.L576L
Silent
11 (13 %)
N
This study
15
c.1960 C>G
p.Q654E
Missense
3 (4 %)
N
This study
Intron 18
c.2392-35 T>C

Intron
9 (11%)
R
[24]
22
c.2829 C>T
p.A943A
Silent
3 (4 %)
R
[24]

TSC2

Exon
Nucleotide change
Codon change
Polymorphism type
Frequency
Reported
Reference

14
c.1593 C>T
p.I531I
Silent
3 (4 %)
R
[26]
Intron 15
c.1717-30 G>A

Intron
2 (2 %)
N
This study
Intron 15
c.1717-27 G>A

Intron
1 (1 %)
N
This study
Intron 21
c.2545+45 T>A

Intron
11 (13 %)
N
This study
23
c.2652 C>T
p.Y884Y
Silent
1 (1 %)
N
This study
26
c.3126 G>T
p.P1042P
Silent
1 (1 %)
R
DKb
Intron 27
c.3285-19 C>T

Intron
1 (1 %)
N
This study
29
c.3475 C>T
p.R1159R
Silent
1 (1 %)
N
This study
33
c.4047 G>A
p.A1349A
Silent
2 (2 %)
N
This study
Intron 33
c.4493+18 G>A

Intron
1 (1 %)
N
This study
Intron 38
c.5069-21 G>A

Intron
1 (1 %)
N
This study
Intron 39
c.5161-9 C>T

Intron
7 (8 %)
N
This study

* Frequence means the number of cases in 84 Taiwanese TSC patients.

a The the Leiden Open (source) Variation Database which was available at http://chromium.liacs.nl/lovd/.

b The database of Dr David Kwiatkowski which was available at http://tsc-project.partners.org/.

Hung et al. BMC Medical Genetics 2006 7:72   doi:10.1186/1471-2350-7-72