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Mean pure-tone averages (PTAs) and average air conduction thresholds from 125 Hz to 8 kHz as a function of age for affected individuals. |
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| Age group (years) |
21–30 |
31–40 |
41–50 |
51–60 |
61–70 |
| Mean ± SD (years) |
25.1 ± 2.6 |
36.6 ± 3 |
50 ± 0 |
58.3 ± 0.5 |
62.5 ± 1.7 |
| Number of ears |
(n = 14) |
(n = 16) |
(n = 4) |
(n = 6) |
(n = 4) |
| PTAs, (dBHL) |
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| right ear |
15.9 (11.9) |
19.6 (13.8) |
45.8 (10.6) |
100.6 (33.7) |
23.3 (14.1) |
| left ear |
19 (19) |
34 (37) |
51.7 (2.3) |
45.5 (9.2) |
41.7 (30.6) |
| Air conduction thresholds |
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| 125 Hz |
17.1 (16.1) |
27.8 (29.8) |
33.7 (4.7) |
60 (47) |
30 (20.4) |
| 250 Hz |
15.3 (15.1) |
25.3 (28.4) |
36.2 (8.5) |
64.2 (43.6) |
26.3 (22.5) |
| 500 Hz |
17.5 (17.5) |
25.9 (28.1) |
47.5 (5) |
73.3 (36.8) |
30 (23.8) |
| 1 kHz |
16.1 (13.7) |
25.6 (28.5) |
46.2 (7.5) |
74.2 (36.1) |
33.7 (21.7) |
| 2 kHz |
18.9 (21.7) |
28.8 (30.1) |
52.5 (11.9) |
71.7 (39.3) |
33.7 (22.8) |
| 4 kHz |
24.6 (19.8) |
49.1 (30.1) |
62.5 (6.4) |
78.3 (32.6) |
50 (10.8) |
| 8 kHz |
32.1 (31.8) |
60.6 (27.6) |
67.5 (8.7) |
89.2 (25.4) |
66.3 (20.2) |
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Data are given as mean (SD). DBHL = decibels hearing level. | |||||
Germain et al. BMC Medical Genetics 2002 3:10 doi:10.1186/1471-2350-3-10 |
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